Congenital dermal sinus and cyst in adulthood.
نویسندگان
چکیده
Dermal sinus tracts are formed during the 26th day of gestation from the incomplete closure of cutaneous ectoderm from neural ectoderm.1-5 As remnants of incomplete neural tube closure, they are often associated with dermoid and epidermoid cysts, spinal cord tethering and spinal fluid drainage.1,2,6-8 As such, dermal sinus tracts are diagnosed during early childhood.2,8 These entities most frequently present in the lumbosacral area and less commonly in the thoracic region.2,8-10 We present a patient with a thoracic dermal sinus tract and an associated intradural dermoid cyst presenting in late adulthood.
منابع مشابه
Congenital dermal sinus.
congenital dermal sinus tract is an uncommon type of spinal dysraphism that results when a focal area of the ectoderm fails to separate from the underlying neuroectoderm, a process termed nondysjunction. Nondysjunction prevents the insertion and subsequent development of mesodermal tissue, which normally separates the spinal cord from the skin. Congenital dermal sinus tracts occur rarely and ar...
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ورودعنوان ژورنال:
- The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques
دوره 36 1 شماره
صفحات -
تاریخ انتشار 2009